ANOMALIES ASSOCIATED WITH ECTOPIA CORDIS

Ref	MA (wks)	Anomalies		Omphalocele	Karyotype	Outcome
		Cardiac	Extracardiac
(1) (1) (1) (1) (1) (1) (1) (1) (1) (1) (2) (3) (4) (5) (6) (6) (6) (6) (7) (8) (9) (10) (11) (12) (13) (14) (15) (16)	28 32 18 31 33 25 23 23 18 19 36 29 34 28 - 28 28 42 33 23 32 21 15 19 18 14 12 28	TOF PFO TOF, ASD Arrhythmia VSD TOF TOF ASD, VSD TOF VSD VSD, PS Unknown TGV, VSD VSD Nil VSD Nil ASD, PDA VSD, PS DORV Unknown ASD, VSD Nil DORV VSD 2 chambers Unknown VSD	Cephalocele Cleft palate Kyphoscoliosis Nil Nuchal edema Ascites Nil Nil Clinodactyly Nil Nil Nil Nil Hydrocephalus Cleft palate Hydrothorax Facial defect Club foot Nil Micropthalmia Nil Esophageal atresia Unknown Kyphoscoliosis Nil Nil Nil Amniotic bands Cystic hygroma Nil	Yes Yes Yes Yes Yes Gastroschisis Yes Yes Yes Yes Yes Yes No No Yes Yes Yes Yes Yes Yes Yes Yes Yes No Yes Yes Yes Yes	47,XX +18 46,XY 46,XY 47,XX +18 46,XX 46,XX 46,XX 46,XX 46,XY 46,XY 46,XY Unknown 46,XY 46,XX Unknown Unknown Unknown Unknown Unknown 46,XY 46,XY 46,XX 47,XX +18 Unknown 46,XX Unknown 46,XY 46,XX	Died Died Died IUD Died TOP TOP TOP TOP TOP Died Died Died Died Died IUD Died Died Died TOP IUD TOP TOP Died Died TOP TOP IUD

KEY:
TOF - Tetralogy of Fallot; ASD - Atrial septal defect; VSD - Ventricular septal defect; PS - Pulmonary stenosis; TGV - Transposition of the Great Vessels; PDA - Patent ductus arteriosis; DORV - Double outlet right ventricle; TOP - Termination of pregnancy; IUD - Intrauterine demise.

REFERENCES

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